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Abstract:

Multifocal motor neuropathy, a rare insidious immune-mediated disorder, features muscular weakness and atrophy, as well as arreflexia, due to nerve conduction block and is often associated with the presence of anti-GM1antibody. We report a patient with a nine-year history of progressive upper limb weakness, misdiagnosed as amyotrophic lateral sclerosis, who responded within hours to intravenous immunoglobulin treatment with full recovery of muscle strength. This case highlights the need to search for conduction block in patients with lower motor neuron involvement.

Registro:

Documento: Artículo
Título:Multifocal motor neuropathy. Immediate response to intravenous immunoglobulin
Autor:Cammarota, A.; Nogues, M.; Rivero, A.; Garcia, H.
Filiación:Depto. de Neurofisiol. Clin., Inst. Invest. Neurologicas Raul C., Buenos Aires, Argentina
Montañeses 2325, 1428 Buenos Aires, Argentina
Palabras clave:Immunoglobulin; Multifocal motor neuropathy; immunoglobulin; immunoglobulin; adult; amyotrophic lateral sclerosis; article; case report; clinical feature; diagnostic error; disease course; human; male; motoneuron; motor neuropathy; muscle strength; nerve block; treatment outcome; amyotrophic lateral sclerosis; differential diagnosis; middle aged; motor neuron disease; nerve conduction; Amyotrophic Lateral Sclerosis; Diagnosis, Differential; Humans; Immunoglobulins, Intravenous; Male; Middle Aged; Motor Neuron Disease; Neural Conduction
Año:2001
Volumen:61
Número:4
Página de inicio:441
Página de fin:444
Título revista:Medicina
Título revista abreviado:Medicina (Argentina)
ISSN:00257680
CODEN:MEDCA
CAS:Immunoglobulins, Intravenous
Registro:https://bibliotecadigital.exactas.uba.ar/collection/paper/document/paper_00257680_v61_n4_p441_Cammarota

Referencias:

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  • Lewis, R.A., Summer, A.J., Brown, M.J., Asbury, A.K., Multifocal demyelinating neuropathy with persistent conduction block (1982) Neurology, 32, pp. 958-964
  • Pestronk, A., Cornblath, D.R., Iiyas, A.A., Baba, H., A treatable multifocal motor neuropathy with antibodies to GM1 ganglioside (1988) Ann Neurol, 24, pp. 73-78
  • Chaudhry, V., Corse, A.M., Cornblath, D.R., Multifocal motor neuropathy: Response to human immune globulin (1993) Ann Neurol, 33, pp. 237-242
  • Traynor, B., Codd, M., Corr, B., Forde, C., Frost, E., Hardiman, O., Amyotrophic lateral sclerosis mimic syndromes. A population- based study (2000) Arch Neurol, 57, pp. 109-113
  • Van Den Berg-Vos, R.M., Van Den Berg, L.H., Franssen, H., Multifocal inflammatory demyelinating neuropathy. A distinct clinical entity? (2000) Neurology, 54, pp. 26-32
  • Kaji, R., Kusunoki, S., Mizutani, K., Oka, N., Kojima, Y., Kohara, N., Kimura, J., Chronic motor axonal neuropathy associated with antibodies monoespecific for N-actylgalactosaminyl GD1a (2000) Muscle & Nerve, 23, pp. 702-706
  • Nobile-Orazio, E., Carpo, M., Legname, G., Meucci, N., Sonnino, S., Scarlato, G., Anti-GM1 IgM antibodies in motor neuron disease and neuropathy (1990) Neurology, 40, pp. 1747-1750
  • Sadiq, S.A., Thomas, F.P., Kilidireas, K., The spectrum of neurologic disease associated with anti-GM1 abtibodies (1990) Neurology, 40, pp. 1067-1072
  • Chaudhry, V., Corse, A.M., Cornblath, D.R., Kuncl, R.W., Freimer, M.L., Griffin, J.W., Multifocal motor neuropathy: Electrodiagnostic features (1994) Muscle & Nerve, 17, pp. 198-205
  • Traynor, B.J., Codd, M.B., Corr, B., Forde, C., Frost, E., Hardiman, O., Amyotrophic lateral sclerosis mimic syndrome: A population-based study (2000) Arch Neurol, 57, pp. 109-113
  • Lewis, R.A., Multifocal motor neuropathy and Lewis Sumner syndrome: Two distinct entities (1999) Muscle & Nerve, 22, pp. 1738-1739

Citas:

---------- APA ----------
Cammarota, A., Nogues, M., Rivero, A. & Garcia, H. (2001) . Multifocal motor neuropathy. Immediate response to intravenous immunoglobulin . Medicina, 61(4), 441-444.
Recuperado de https://bibliotecadigital.exactas.uba.ar/collection/paper/document/paper_00257680_v61_n4_p441_Cammarota [ ]
---------- CHICAGO ----------
Cammarota, A., Nogues, M., Rivero, A., Garcia, H. "Multifocal motor neuropathy. Immediate response to intravenous immunoglobulin " . Medicina 61, no. 4 (2001) : 441-444.
Recuperado de https://bibliotecadigital.exactas.uba.ar/collection/paper/document/paper_00257680_v61_n4_p441_Cammarota [ ]
---------- MLA ----------
Cammarota, A., Nogues, M., Rivero, A., Garcia, H. "Multifocal motor neuropathy. Immediate response to intravenous immunoglobulin " . Medicina, vol. 61, no. 4, 2001, pp. 441-444.
Recuperado de https://bibliotecadigital.exactas.uba.ar/collection/paper/document/paper_00257680_v61_n4_p441_Cammarota [ ]
---------- VANCOUVER ----------
Cammarota, A., Nogues, M., Rivero, A., Garcia, H. Multifocal motor neuropathy. Immediate response to intravenous immunoglobulin . Medicina (Argentina). 2001;61(4):441-444.
Available from: https://bibliotecadigital.exactas.uba.ar/collection/paper/document/paper_00257680_v61_n4_p441_Cammarota [ ]